public_id

FDB022796

IUPAC 名称

3-(tetradec-5-enoyloxy)-4-(trimethylazaniumyl)butanoate

描述

Tetradecenoylcarnitine (C14:1) is the most characteristic metabolic marker of very long chain acyl-dehydrogenase (VLCAD) deficiency (PubMed ID 11433098 ); beta-Oxidation of long-chain fatty acids provides the major source of energy in the heart. Defects in enzymes of the beta-oxidation pathway cause sudden, unexplained death in childhood, acute hepatic encephalopathy or liver failure, skeletal myopathy, and cardiomyopathy. ( PubMed ID 7479827 ) [HMDB]

CAS号

835598-21-5

异构

CCCCCCCCC=CCCCC(=O)OC(CC([O-])=O)C[N+](C)(C)C

InChI标识符

InChI=1S/C21H39NO4/c1-5-6-7-8-9-10-11-12-13-14-15-16-21(25)26-19(17-20(23)24)18-22(2,3)4/h12-13,19H,5-11,14-18H2,1-4H3

键

NNCBVXBBLABOCB-UHFFFAOYSA-N

平均分子量

369.287908741

id

22959

含有化合物的食物

食物id	食物名称
353	Mule deer
595	Mountain hare
632	Milk (Cow)
358	Mallard duck
383	Horse
378	Guinea hen
373	Greylag goose
451	European rabbit
365	Emu
364	Elk
549	Domestic pig
541	Domestic goat
535	Deer
624	Columbidae (Dove, Pigeon)
334	Chicken
506	Cattle (Beef, Veal)
316	Buffalo
303	Bison
542	Beefalo
590	Anatidae