Propionylcarnitine,化合物成分

Propionylcarnitine

public_id

FDB022268

IUPAC 名称

3-(propanoyloxy)-4-(trimethylazaniumyl)butanoate

描述

Propionylcarnitine is present in high abundance in the urine of patients with Methylmalonyl-CoA mutase (MUT) deficiency, (together with Methylmalonic acid). MUT is a mitochondrial enzyme that catalyzes the isomerization of methylmalonyl-CoA to succinyl-CoA (OMIM 609058 ) [HMDB]

CAS号

17298-37-2

异构

CCC(=O)OC(CC([O-])=O)C[N+](C)(C)C

InChI标识符

InChI=1S/C10H19NO4/c1-5-10(14)15-8(6-9(12)13)7-11(2,3)4/h8H,5-7H2,1-4H3

键

UFAHZIUFPNSHSL-UHFFFAOYSA-N

平均分子量

217.131408101

id

22431

含有化合物的食物

食物id	食物名称
383	Horse
378	Guinea hen
373	Greylag goose
451	European rabbit
365	Emu
364	Elk
549	Domestic pig
541	Domestic goat
535	Deer
924	Cow milk, pasteurized, vitamin D added, 3.25% fat
923	Cow milk, pasteurized, vitamin A + D added, 2% fat
922	Cow milk, pasteurized, vitamin A + D added, 1% fat
921	Cow milk, pasteurized, vitamin A + D added, 0% fat
624	Columbidae (Dove, Pigeon)
334	Chicken
506	Cattle (Beef, Veal)
316	Buffalo
303	Bison
542	Beefalo
590	Anatidae