L-Octanoylcarnitine
public_id
FDB022246
IUPAC 名称
(3R)-3-(octanoyloxy)-4-(trimethylazaniumyl)butanoate
描述
L-Octanoylcarnitine is the physiologically active form of octanoylcarnitine. (PMID 11274033) Octanoylcarnitine is detected in medium-chain acyl-CoA dehydrogenase (MCAD) deficiency . MCAD is characterized by intolerance to prolonged fasting, recurrent episodes of hypoglycemic coma with medium-chain dicarboxylic aciduria, impaired ketogenesis, and low plasma and tissue carnitine levels. (OMIM 201450) [HMDB]
CAS号
25243-95-2
异构
CCCCCCCC(=O)O[C@H](CC([O-])=O)C[N+](C)(C)C
InChI标识符
InChI=1S/C15H29NO4/c1-5-6-7-8-9-10-15(19)20-13(11-14(17)18)12-16(2,3)4/h13H,5-12H2,1-4H3/t13-/m1/s1
CXTATJFJDMJMIY-CYBMUJFWSA-N
平均分子量
287.209658421
id
22409
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