public_id

FDB022204

IUPAC 名称

(2S)-2-(3-methylbutanamido)pentanedioic acid

描述

Isovalerylglutamic acid is an unusual mtabolite that has been found in the urine of patients with Isovaleric Acidemia due to Isovaleryl-CoA Dehydrogenase Deficiency (OMMBID: The Metabolic and Molecular Bases of Inherited Disease, Ch.93: Branched Chain Organic Acidurias) and in Multiple acyl-Co A dehydrogenation deficiency (MADD) (PMID 6862997) [HMDB]. Isovalerylglutamate is a biomarker for the consumption of cheese.

CAS号

80154-63-8

异构

CC(C)CC(=O)N[C@@H](CCC(O)=O)C(O)=O

InChI标识符

InChI=1S/C10H17NO5/c1-6(2)5-8(12)11-7(10(15)16)3-4-9(13)14/h6-7H,3-5H2,1-2H3,(H,11,12)(H,13,14)(H,15,16)/t7-/m0/s1

键

HCVIJONZMYVLAW-ZETCQYMHSA-N

平均分子量

231.110672659

id

22367

含有化合物的食物

食物id	食物名称
430	Ostrich
353	Mule deer
595	Mountain hare
358	Mallard duck
383	Horse
378	Guinea hen
373	Greylag goose
451	European rabbit
365	Emu
364	Elk
549	Domestic pig
541	Domestic goat
535	Deer
624	Columbidae (Dove, Pigeon)
334	Chicken
506	Cattle (Beef, Veal)
316	Buffalo
303	Bison
542	Beefalo
590	Anatidae