胆汁淤积，良性复发性肝内，2
基因病名称(英)
Cholestasis, benign recurrent intrahepatic, 2
关键字(英)
Intrahepatic cholestasis
统计
reviewed:1; annotated:0
交叉引用
605479,C2608083,D002780
描述(英)
A disorder characterized by intermittent episodes of cholestasis without progression to liver failure. There is initial elevation of serum bile acids, followed by cholestatic jaundice which generally spontaneously resolves after periods of weeks to months. The cholestatic attacks vary in severity and duration. Patients are asymptomatic between episodes, both clinically and biochemically.
描述
一种以间歇性胆汁淤积而不进展为肝功能衰竭为特征的疾病。初始血清胆汁酸升高，随后出现胆汁淤积性黄疸，通常在数周至数月后自行消退。胆汁淤积发作的严重程度和持续时间各不相同。患者在发作之间没有临床症状和生化症状。