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Hypoacetylaspartia
SMPDB_ID
SMP0000192
PW_ID
PW000094
图片
主题
Disease
描述
Hypoacetylaspartia is a result of a defect in L-aspartate-N-acetyltransferase which results in a strongly decreased concentration of N-acetyl-L-aspartic acid according to the in vivo spectrum of the brain.
代谢物
SMPDB ID
代谢物id
代谢物的名字
SMP0000192
PW_C000396
L-Arginine
SMP0000192
PW_C000662
Ureidosuccinic acid
SMP0000192
PW_C000862
Carbamoyl phosphate
SMP0000192
PW_C000423
Magnesium
SMP0000192
PW_C001104
Phosphate
SMP0000192
PW_C000936
Guanosine diphosphate
SMP0000192
PW_C000114
Inosinic acid
SMP0000192
PW_C000986
Guanosine triphosphate
SMP0000192
PW_C001005
Zinc (II) ion
SMP0000192
PW_C000029
Acetic acid
SMP0000192
PW_C000649
N-Acetyl-L-aspartic acid
SMP0000192
PW_C000964
FAD
SMP0000192
PW_C001065
Oxygen
SMP0000192
PW_C002766
D-Aspartic acid
SMP0000192
PW_C000088
Fumaric acid
SMP0000192
PW_C000413
Adenylsuccinic acid
SMP0000192
PW_C000035
Ammonia
SMP0000192
PW_C000148
Oxalacetic acid
SMP0000192
PW_C000036
Argininosuccinic acid
SMP0000192
PW_C000723
Citrulline
SMP0000192
PW_C000110
L-Asparagine
SMP0000192
PW_C000170
Pyrophosphate
SMP0000192
PW_C000032
Adenosine monophosphate
SMP0000192
PW_C001420
Water
SMP0000192
PW_C000500
L-Glutamine
SMP0000192
PW_C000414
Adenosine triphosphate
SMP0000192
PW_C001316
Carbon dioxide
SMP0000192
PW_C000123
L-Aspartic acid
SMP0000192
PW_C001148
Pyridoxal 5'-phosphate
SMP0000192
PW_C000095
L-Glutamic acid
SMP0000192
PW_C006753
Malonic semialdehyde
SMP0000192
PW_C000134
Oxoglutaric acid
SMP0000192
PW_C000040
beta-Alanine
SMP0000192
PW_C001783
Hydrogen peroxide
蛋白质
SMPDB ID
蛋白质id
蛋白质的名字
SMP0000192
Q96RQ9
L-amino-acid oxidase
SMP0000192
P04424
Argininosuccinate lyase
SMP0000192
Q7L266
Isoaspartyl peptidase/L-asparaginase
SMP0000192
P27708
CAD protein
SMP0000192
Q8N142
Adenylosuccinate synthetase isozyme 1
SMP0000192
P45381
Aspartoacylase
SMP0000192
Q99489
D-aspartate oxidase
SMP0000192
P30566
Adenylosuccinate lyase
SMP0000192
P14868
Aspartate--tRNA ligase, cytoplasmic
SMP0000192
P00966
Argininosuccinate synthase
SMP0000192
O43776
Asparagine--tRNA ligase, cytoplasmic
SMP0000192
P08243
Asparagine synthetase [glutamine-hydrolyzing]
SMP0000192
Q99259
Glutamate decarboxylase 1
SMP0000192
P80404
4-aminobutyrate aminotransferase, mitochondrial
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