Orotic acid
名称
Orotic acid
case号
65-86-1
化学分类
Organic compounds
子类
Organoheterocyclic compounds
细胞类型
Diazines
子类
Pyrimidines and pyrimidine derivatives
化学架构
Aromatic heteromonocyclic compounds
细胞
Cytoplasm|
生物样本
Amniotic Fluid|Blood|Feces|Saliva|Urine|
组织
Liver|Pancreas|Placenta|
正常浓度
biospecimen:Amniotic Fluid

concentration_value:0.27 +/- 0.25

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.89 +/- 0.63

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:2.874 +/- 8.0460

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:5.0 +/- 0.4

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Children (6 - 18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<20

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:9.9 +/- 7.1

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.26-3.20

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.5-3.3

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value: 0.49 - 3.44

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.0-3.2

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.63 +/- 0.21

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.3-5.3

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.07

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0-5

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0-5

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.23 +/- 0.13

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.16 +/- 0.12

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<4.33

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.4

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.061 +/- 0.003

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.05 +/- 1.22

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.0800-0.440

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.05 +/- 1.22

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<3

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.0350-0.260

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:38.506 +/- 91.954

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Uremia

biospecimen:Blood

concentration_value:0.94 +/- 0.78

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Canavan disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal Cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Both

patient_information:Crohns disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Both

patient_information:Ulcerative colitis

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Unclassified IBD

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Crohns disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Ulcerative colitis

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Urine

concentration_value:427.09-2989.61

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:1.4-3.2

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Male

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:1000

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:293.333-573.333

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:5.6

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:8.24

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Female

patient_information:Orotic aciduria I

biospecimen:Urine

concentration_value:66.667-640

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:Orotic Aciduria hereditary

biospecimen:Urine

concentration_value:59-282

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hyperornithinemia鈥揌yperammonemia-Homocitrullinuria syndrome

biospecimen:Urine

concentration_value:44.16(0.72-642.79)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Lysinuric protein intolerance (LPI) syndrome

biospecimen:Urine

concentration_value:2-2800

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:OTC-deficiency

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Bladder cancer

biospecimen:Urine

concentration_value:253.2 +/- 540.0

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:OTC-deficiency

biospecimen:Urine

concentration_value:6.11 +/- 5.48

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Canavan disease

biospecimen:Urine

concentration_value:0.720-2339

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:N-acetylglutamate synthetase deficiency

biospecimen:Urine

concentration_value:5.4

concentration_units:umol/mmol creatinine

patient_age:Newborn (0-30 days old)

patient_sex:Male

patient_information:Phosphoenolpyruvate Carboxykinase Deficiency 1, Cytosolic

biospecimen:Urine

concentration_value:>20

concentration_units:umol/mmol creatinine

patient_age:Newborn (0-30 days old)

patient_sex:Male

patient_information:Ornithine transcarbamylase deficiency

疾病参考
Canavan disease|Uremia|Colorectal cancer|Crohn's disease|Ulcerative colitis|Ornithine transcarbamylase deficiency|Orotic aciduria I|N-acetylglutamate synthetase deficiency|Hyperornithinemia-hyperammonemia-homocitrullinuria|Lysinuric protein intolerance|Phosphoenolpyruvate Carboxykinase Deficiency 1, Cytosolic|
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