Oxoadipic acid
名称
Oxoadipic acid
case号
3184-35-8
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Keto acids and derivatives
子类
Medium-chain keto acids and derivatives
化学架构
Aliphatic acyclic compounds
细胞
Mitochondria|
生物样本
Blood|Urine|
组织
正常浓度
biospecimen:Blood

concentration_value:

concentration_units:

subject_age:

subject_sex:

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.2

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.17 (0.02-0.57)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:0.21 (0.04-0.81)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:1.3 (1.0-1.5)

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Urine

concentration_value:520-970

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:2-Aminoadipic aciduria

biospecimen:Urine

concentration_value:62

concentration_units:umol/mmol creatinine

patient_age:Adolescent (13-18 years old)

patient_sex:Male

patient_information:alpha-Ketoadipic Aciduria

biospecimen:Urine

concentration_value:20-120

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:alpha-Aminoadipic aciduria

biospecimen:Urine

concentration_value:456

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:alpha-ketoadipic aciduria

biospecimen:Urine

concentration_value:135

concentration_units:umol/mmol creatinine

patient_age:Newborn (0-30 days old)

patient_sex:Not Specified

patient_information:alpha-ketoadipic aciduria

疾病参考
2-Ketoadipic acidemia|Alpha-aminoadipic aciduria|2-Aminoadipic aciduria|
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