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Oxoadipic acid
子类
Organic acids and derivatives
细胞类型
Keto acids and derivatives
子类
Medium-chain keto acids and derivatives
化学架构
Aliphatic acyclic compounds
正常浓度
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:
subject_sex:
subject_condition:Normal
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.2
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.17 (0.02-0.57)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0.21 (0.04-0.81)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:1.3 (1.0-1.5)
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Urine
concentration_value:520-970
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:2-Aminoadipic aciduria
biospecimen:Urine
concentration_value:62
concentration_units:umol/mmol creatinine
patient_age:Adolescent (13-18 years old)
patient_sex:Male
patient_information:alpha-Ketoadipic Aciduria
biospecimen:Urine
concentration_value:20-120
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Not Specified
patient_information:alpha-Aminoadipic aciduria
biospecimen:Urine
concentration_value:456
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Not Specified
patient_information:alpha-ketoadipic aciduria
biospecimen:Urine
concentration_value:135
concentration_units:umol/mmol creatinine
patient_age:Newborn (0-30 days old)
patient_sex:Not Specified
patient_information:alpha-ketoadipic aciduria
疾病参考
2-Ketoadipic acidemia|Alpha-aminoadipic aciduria|2-Aminoadipic aciduria|