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Oxoglutaric acid
子类
Organic acids and derivatives
细胞类型
Keto acids and derivatives
子类
Gamma-keto acids and derivatives
化学架构
Aliphatic acyclic compounds
细胞
Endoplasmic reticulum|Extracellular|Mitochondria|Peroxisome|
生物样本
Blood|Breast Milk|Cellular Cytoplasm|Cerebrospinal Fluid (CSF)|Feces|Saliva|Urine|
正常浓度
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:7.0 (0.0-23.0)
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:8.6 +/- 2.6
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:9.3 +/- 2.3
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:8.9 +/- 2.7
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:4-13
concentration_units:uM
subject_age:Not Specified
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Blood
concentration_value:20.7 +/- 2.5
concentration_units:uM
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Breast Milk
concentration_value:41.0 +/- 16.1
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Cellular Cytoplasm
concentration_value:320 (290-350)
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:5 +/- 4
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:2.1 +/- 0.7
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:8.9 +/- 3.4
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:16-Feb
concentration_units:uM
subject_age:Not Specified
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:2.0 +/- 2.0
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:4.80 (3.40-6.20)
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:5.27 +/- 3.61
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:1.53 +/- 1.18
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Saliva
concentration_value:1.64 +/- 3.47
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:2.65 +/- 1.07
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Saliva
concentration_value:2.65 +/- 1.07
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Saliva
concentration_value:3.78 +/- 2.33
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:<110
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:32.164 +/- 9.964
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:30.79-398.2
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:12-20
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:90.83(45.64-331.1)
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:<150
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:104.8(30.21-413.8)
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:2.87 (0.18-14.3)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:2.98 (0.42-18.3)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:23.6
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:29.893 +/- 15.594
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<60
concentration_units:umol/mmol creatinine
subject_age:Not Specified
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<75
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<95
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:<115
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<350
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0-25.3
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:14.8-64.7
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:4.3-36.3
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:7.5-28.9
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:8.90-17.12
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:4.2 +/- 1.97
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:24 (4-74)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:150.5 (10.0-836.3)
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:236.9 (8.0-631.4)
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:21.4 (4.9-123.8)
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:25.6 (10.2-146.0)
concentration_units:umol/mmol creatinine
subject_age:Adolescent (13-18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:15.477-154.773
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:7-11
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:4.8 (2.0-17.0)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:2.2-8.2
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.083 +/- 0.002
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.548-39.467
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 13 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:43.46 +/- 53.46
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<79
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:> 0.658
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:160-590
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:3.4 (1.4-12.5)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Schizophrenia
biospecimen:Blood
concentration_value:17-37
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:2-Ketoglutarate dehydrogenase complex deficiency
biospecimen:Blood
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Schizophrenia
biospecimen:Cellular Cytoplasm
concentration_value:150 (144-156)
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Anoxia
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:3.600-12.800
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:2-Ketoglutarate dehydrogenase complex deficiency
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Colorectal Cancer
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Immunoglobulin A nephropathy (IgAN) progressor
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Colorectal cancer
biospecimen:Urine
concentration_value:1374
concentration_units:umol/mmol creatinine
patient_age:Newborn (0-30 days old)
patient_sex:Female
patient_information:Deafness, Onychodystrophy, Osteodystrophy, Mental Retardation, and Seizures Syndrome
biospecimen:Urine
concentration_value:28.849 +/- 8.834
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Not Specified
patient_information:Eosinophilic esophagitis
biospecimen:Urine
concentration_value:39.88 +/- 30.024
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Not Specified
patient_information:Gastroesophageal reflux disease
biospecimen:Urine
concentration_value:30-1600
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:2-Ketoglutarate dehydrogenase complex deficiency
biospecimen:Urine
concentration_value:24.882 +/- 26.016
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Not Specified
patient_information:Eosinophilic esophagitis
biospecimen:Urine
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Schizophrenia
biospecimen:Urine
concentration_value:100-166
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Hyperinsulinism-hyperammonemia syndrome
biospecimen:Urine
concentration_value:149-247
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Hyperinsulinism-hyperammonemia syndrome
biospecimen:Urine
concentration_value:15-107
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Hyperinsulinism-hyperammonemia syndrome
biospecimen:Urine
concentration_value:1172.1
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Fumarase deficiency
biospecimen:Urine
concentration_value:385.200-1367.300
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Fumarase deficiency
biospecimen:Urine
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Bladder cancer
biospecimen:Urine
concentration_value:673.261-2970.0885
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Both
patient_information:Amish lethal microcephaly
biospecimen:Urine
concentration_value:1119.294
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Dihydrolipoamide Dehydrogenase Deficiency
biospecimen:Urine
concentration_value:26.667
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Male
patient_information:D-2-Hydroxyglutaric aciduria
biospecimen:Urine
concentration_value:46.432
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Male
patient_information:D-2-Hydroxyglutaric aciduria
biospecimen:Urine
concentration_value:193.466
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Male
patient_information:D-2-Hydroxyglutaric aciduria
biospecimen:Urine
concentration_value:6224
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Male
patient_information:Lipoyltransferase 1 Deficiency
biospecimen:Urine
concentration_value:101.0 (50.0-152.0)
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:2-Ketoglutarate dehydrogenase complex deficiency
biospecimen:Urine
concentration_value:875.0 (150.0-1600.0)
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:2-Ketoglutarate Dehydrogenase Complex Deficiency
疾病参考
Schizophrenia|Anoxia|Colorectal cancer|2-Ketoglutarate dehydrogenase complex deficiency|Eosinophilic esophagitis|D-2-hydroxyglutaric aciduria|Hyperinsulinism-hyperammonemia syndrome|Fumarase deficiency|Amish lethal microcephaly|Deafness, Onychodystrophy, Osteodystrophy, Mental Retardation, and Seizures Syndrome|Dihydrolipoamide Dehydrogenase Deficiency|Lipoyltransferase 1 Deficiency|