Oxoglutaric acid
名称
Oxoglutaric acid
case号
328-50-7
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Keto acids and derivatives
子类
Gamma-keto acids and derivatives
化学架构
Aliphatic acyclic compounds
细胞
Endoplasmic reticulum|Extracellular|Mitochondria|Peroxisome|
生物样本
Blood|Breast Milk|Cellular Cytoplasm|Cerebrospinal Fluid (CSF)|Feces|Saliva|Urine|
组织
Placenta|
正常浓度
biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:7.0 (0.0-23.0)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:8.6 +/- 2.6

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:9.3 +/- 2.3

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:8.9 +/- 2.7

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:4-13

concentration_units:uM

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:20.7 +/- 2.5

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Breast Milk

concentration_value:41.0 +/- 16.1

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Cellular Cytoplasm

concentration_value:320 (290-350)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:5 +/- 4

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:2.1 +/- 0.7

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:8.9 +/- 3.4

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:16-Feb

concentration_units:uM

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:2.0 +/- 2.0

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:4.80 (3.40-6.20)

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:5.27 +/- 3.61

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:1.53 +/- 1.18

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Saliva

concentration_value:1.64 +/- 3.47

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:2.65 +/- 1.07

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Saliva

concentration_value:2.65 +/- 1.07

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Saliva

concentration_value:3.78 +/- 2.33

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:<110

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:32.164 +/- 9.964

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:30.79-398.2

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:12-20

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:90.83(45.64-331.1)

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:<150

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:104.8(30.21-413.8)

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:2.87 (0.18-14.3)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:2.98 (0.42-18.3)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:23.6

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:29.893 +/- 15.594

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<60

concentration_units:umol/mmol creatinine

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:<75

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<95

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:<115

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<350

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:0-25.3

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:14.8-64.7

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:4.3-36.3

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:7.5-28.9

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:8.90-17.12

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:4.2 +/- 1.97

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:24 (4-74)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:150.5 (10.0-836.3)

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:236.9 (8.0-631.4)

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:21.4 (4.9-123.8)

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:25.6 (10.2-146.0)

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13-18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:15.477-154.773

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:7-11

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:4.8 (2.0-17.0)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.2-8.2

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.083 +/- 0.002

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.548-39.467

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:43.46 +/- 53.46

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<79

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:> 0.658

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:160-590

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:3.4 (1.4-12.5)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Blood

concentration_value:17-37

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:2-Ketoglutarate dehydrogenase complex deficiency

biospecimen:Blood

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Cellular Cytoplasm

concentration_value:150 (144-156)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Anoxia

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:3.600-12.800

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:2-Ketoglutarate dehydrogenase complex deficiency

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal Cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Immunoglobulin A nephropathy (IgAN) progressor

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Urine

concentration_value:1374

concentration_units:umol/mmol creatinine

patient_age:Newborn (0-30 days old)

patient_sex:Female

patient_information:Deafness, Onychodystrophy, Osteodystrophy, Mental Retardation, and Seizures Syndrome

biospecimen:Urine

concentration_value:28.849 +/- 8.834

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Eosinophilic esophagitis

biospecimen:Urine

concentration_value:39.88 +/- 30.024

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Gastroesophageal reflux disease

biospecimen:Urine

concentration_value:30-1600

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:2-Ketoglutarate dehydrogenase complex deficiency

biospecimen:Urine

concentration_value:24.882 +/- 26.016

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Eosinophilic esophagitis

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Urine

concentration_value:100-166

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hyperinsulinism-hyperammonemia syndrome

biospecimen:Urine

concentration_value:149-247

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Hyperinsulinism-hyperammonemia syndrome

biospecimen:Urine

concentration_value:15-107

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Hyperinsulinism-hyperammonemia syndrome

biospecimen:Urine

concentration_value:1172.1

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:Fumarase deficiency

biospecimen:Urine

concentration_value:385.200-1367.300

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:Fumarase deficiency

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Bladder cancer

biospecimen:Urine

concentration_value:673.261-2970.0885

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Both

patient_information:Amish lethal microcephaly

biospecimen:Urine

concentration_value:1119.294

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:Dihydrolipoamide Dehydrogenase Deficiency

biospecimen:Urine

concentration_value:26.667

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:D-2-Hydroxyglutaric aciduria

biospecimen:Urine

concentration_value:46.432

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:D-2-Hydroxyglutaric aciduria

biospecimen:Urine

concentration_value:193.466

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:D-2-Hydroxyglutaric aciduria

biospecimen:Urine

concentration_value:6224

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Lipoyltransferase 1 Deficiency

biospecimen:Urine

concentration_value:101.0 (50.0-152.0)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:2-Ketoglutarate dehydrogenase complex deficiency

biospecimen:Urine

concentration_value:875.0 (150.0-1600.0)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:2-Ketoglutarate Dehydrogenase Complex Deficiency

疾病参考
Schizophrenia|Anoxia|Colorectal cancer|2-Ketoglutarate dehydrogenase complex deficiency|Eosinophilic esophagitis|D-2-hydroxyglutaric aciduria|Hyperinsulinism-hyperammonemia syndrome|Fumarase deficiency|Amish lethal microcephaly|Deafness, Onychodystrophy, Osteodystrophy, Mental Retardation, and Seizures Syndrome|Dihydrolipoamide Dehydrogenase Deficiency|Lipoyltransferase 1 Deficiency|

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