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Phenylpyruvic acid
细胞类型
Benzene and substituted derivatives
子类
Phenylpyruvic acid derivatives
化学架构
Aromatic homomonocyclic compounds
细胞
Cytoplasm|Mitochondria|
正常浓度
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0.5 +/- 0.1
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:5
concentration_units:uM
subject_age:Children (1 - 13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.17 (0.05-0.67)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0.24 (0.10-0.76)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.00064 +/- 0.000544
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<2
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.138 +/- 0.207
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.207 +/- 0.275
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.207 +/- 0.344
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.25 +/- 0.43
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:50.0 (40.0-60.0)
concentration_units:uM
patient_age:Newborn (0-30 days old)
patient_sex:Both
patient_information:Phenylketonuria
biospecimen:Blood
concentration_value:1.4 +/- 0.2
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Primary biliary cirrhosis
biospecimen:Urine
concentration_value:7796.386
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Phenylketonuria
biospecimen:Urine
concentration_value:31047.8
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Male
patient_information:Phenylketonuria
biospecimen:Urine
concentration_value:255.518 +/- 250.00780
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Phenylketonuria
biospecimen:Urine
concentration_value:735.560 +/- 528.253
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Phenylketonuria
biospecimen:Urine
concentration_value:882.948 +/- 741.0699
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Phenylketonuria
biospecimen:Urine
concentration_value:146.6 +/- 244.6
concentration_units:umol/mmol creatinine
patient_age:Newborn (0-30 days old)
patient_sex:Both
patient_information:Phenylketonuria
疾病参考
Phenylketonuria|Primary biliary cirrhosis|