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L-Cystine
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
细胞
Cytoplasm|Extracellular|
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Urine|
正常浓度
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:17-98
concentration_units:uM
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Blood
concentration_value:26-77
concentration_units:uM
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:130.0 +/- 20.0
concentration_units:uM
subject_age:Newborn (0-30 days old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Blood
concentration_value:26-61
concentration_units:uM
subject_age:Infant (1 - 3 months old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:91.0 +/- 20.0
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Blood
concentration_value:8-68
concentration_units:uM
subject_age:Children (3 months - 6 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:96.0 +/- 19.0
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:15-65
concentration_units:uM
subject_age:Children (6 - 18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:118.0 +/- 17.0
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Blood
concentration_value:109.0 +/- 24.0
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Blood
concentration_value:87.0 +/- 13.0
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Blood
concentration_value:62.9 +/- 27.8
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:109.0 +/- 18.0
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Blood
concentration_value:107.0 +/- 23.0
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0.1 +/- 0.1
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0.29 +/- 0.27
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0-1.5
concentration_units:uM
subject_age:Children (0 - 10 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0-1.5
concentration_units:uM
subject_age:Adolescent (>11 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Not Specified
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<6.33
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:3.618 (1.316-5.921)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:10.5
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<11.76
concentration_units:umol/mmol creatinine
subject_age:Adolescent (13-18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:2.92-54.16
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:12.10 - 43.64
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:6.22 - 26.12
concentration_units:umol/mmol creatinine
subject_age:Infant (1 - 6 months old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:5.09 - 15.60
concentration_units:umol/mmol creatinine
subject_age:Infant (6 months - <1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:3.84 - 13.23
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 2 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:2.71 - 15.60
concentration_units:umol/mmol creatinine
subject_age:Children (2 - 4 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:2.71 - 12.10
concentration_units:umol/mmol creatinine
subject_age:Children (4 - 13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.70 - 20.92
concentration_units:umol/mmol creatinine
subject_age:Adolescent (13 - 21 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.70 - 17.86
concentration_units:umol/mmol creatinine
subject_age:Adult (>21 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.13-11.086
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:10.05 +/- 28.34
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:12.5 (5.0-24.6)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.36-57.00
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:0.15 (0.1-0.2)
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:3.6 +/- 2.0
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:9.0 +/- 3.0
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:7.0 +/- 3.0
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:2.61 +/- 1.42
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:10.351 +/- 4.234
concentration_units:umol/mmol creatinine
subject_age:Not Specified
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:10.351 +/- 4.234
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:27.821 +/- 17.962
concentration_units:umol/mmol creatinine
subject_age:Children (1 - 13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:5.314-22.612
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:1.24-15.045
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:2-51
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<14.71
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:89.32 +/- 56.53
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:128.89 +/- 56.53
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:152.63 +/- 76.88
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Colorectal cancer
biospecimen:Blood
concentration_value:28.6 (24.2-33.0)
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Juvenile myoclonic epilepsy (JME)
biospecimen:Blood
concentration_value:30.1 (24.5-35.7)
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Acute seizures
biospecimen:Blood
concentration_value:37.2 (34.6-39.8)
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Refractory localization-related epilepsy (RLE)
biospecimen:Blood
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Schizophrenia
biospecimen:Blood
concentration_value:209.0 +/- 46.0
concentration_units:uM
patient_age:Elderly (>65 years old)
patient_sex:Both
patient_information:Alzheimer's Disease
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0.31 +/- 0.06
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Parkinson's Disease
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:7.8 +/- 2.5
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Alzheimer's disease
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Colorectal cancer
biospecimen:Urine
concentration_value:136.5-79.36
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Male
patient_information:Cystinuria
biospecimen:Urine
concentration_value:90.800-558.500
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystinuria
biospecimen:Urine
concentration_value:140.0813-306.845
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Not Specified
patient_information:Cystinuria Type I/III
biospecimen:Urine
concentration_value:100.0581-246.245
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Not Specified
patient_information:Cystinuria Type I/III
biospecimen:Urine
concentration_value:111.929-196.724
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Not Specified
patient_information:Cystinuria Type II
biospecimen:Urine
concentration_value:11.306-67.836
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Not Specified
patient_information:Cystinuria Type III
biospecimen:Urine
concentration_value:65.0 (30.0-100.0)
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystinuria
biospecimen:Urine
concentration_value:575.0 (150.0 -1000.0)
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Cystinuria
biospecimen:Urine
concentration_value:> 117
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystinuria
biospecimen:Urine
concentration_value:908-5585
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Hyperlysinuria
biospecimen:Urine
concentration_value:4.423-24.136
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Dibasic Amino Aciduria I
biospecimen:Urine
concentration_value:6.681-21.125
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Dibasic Amino Aciduria I
biospecimen:Urine
concentration_value:0
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Not Specified
patient_information:Molybdenum cofactor deficiency
biospecimen:Urine
concentration_value:7
concentration_units:umol/mmol creatinine
patient_age:Newborn (0-30 days old)
patient_sex:Not Specified
patient_information:Molybdenum cofactor deficiency
biospecimen:Urine
concentration_value:135.900-156.400
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Not Specified
patient_information:Fumaric aciduria
biospecimen:Urine
concentration_value:17.486 +/- 14.104
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Not Specified
patient_information:Eosinophilic esophagitis
biospecimen:Urine
concentration_value:463.1
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystinuria
biospecimen:Urine
concentration_value:5.975-24.136
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Female
patient_information:Hyperdibasic aminoaciduria I
biospecimen:Urine
concentration_value:6.681-2.305
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Hyperdibasic aminoaciduria I
biospecimen:Urine
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Schizophrenia
biospecimen:Urine
concentration_value:72.03 +/- 12.0
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Alzheimer's disease
疾病参考
Juvenile myoclonic epilepsy|Acute seizures|Refractory localization-related epilepsy|Alzheimer's disease|Colorectal cancer|Schizophrenia|Parkinson's disease|Cystinuria|Eosinophilic esophagitis|Molybdenum cofactor deficiency|Fumarase deficiency|Hyperdibasic aminoaciduria I|Hyperlysinuria|