L-Cystine
名称
L-Cystine
case号
56-89-3
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
细胞
Cytoplasm|Extracellular|
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Urine|
组织
All Tissues|Placenta|
正常浓度
biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:17-98

concentration_units:uM

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:26-77

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:130.0 +/- 20.0

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:26-61

concentration_units:uM

subject_age:Infant (1 - 3 months old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:91.0 +/- 20.0

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Blood

concentration_value:8-68

concentration_units:uM

subject_age:Children (3 months - 6 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:96.0 +/- 19.0

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:15-65

concentration_units:uM

subject_age:Children (6 - 18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:118.0 +/- 17.0

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Blood

concentration_value:109.0 +/- 24.0

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Blood

concentration_value:87.0 +/- 13.0

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:62.9 +/- 27.8

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:109.0 +/- 18.0

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Blood

concentration_value:107.0 +/- 23.0

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.1 +/- 0.1

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.29 +/- 0.27

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0-1.5

concentration_units:uM

subject_age:Children (0 - 10 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0-1.5

concentration_units:uM

subject_age:Adolescent (>11 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Not Specified

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<6.33

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:3.618 (1.316-5.921)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:10.5

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<11.76

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13-18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:2.92-54.16

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:12.10 - 43.64

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:6.22 - 26.12

concentration_units:umol/mmol creatinine

subject_age:Infant (1 - 6 months old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:5.09 - 15.60

concentration_units:umol/mmol creatinine

subject_age:Infant (6 months - <1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:3.84 - 13.23

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 2 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.71 - 15.60

concentration_units:umol/mmol creatinine

subject_age:Children (2 - 4 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.71 - 12.10

concentration_units:umol/mmol creatinine

subject_age:Children (4 - 13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.70 - 20.92

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13 - 21 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.70 - 17.86

concentration_units:umol/mmol creatinine

subject_age:Adult (>21 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.13-11.086

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:10.05 +/- 28.34

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:12.5 (5.0-24.6)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.36-57.00

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.15 (0.1-0.2)

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:3.6 +/- 2.0

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:9.0 +/- 3.0

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:7.0 +/- 3.0

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.61 +/- 1.42

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:10.351 +/- 4.234

concentration_units:umol/mmol creatinine

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:10.351 +/- 4.234

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:27.821 +/- 17.962

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:5.314-22.612

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:1.24-15.045

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2-51

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<14.71

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:89.32 +/- 56.53

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:128.89 +/- 56.53

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:152.63 +/- 76.88

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Blood

concentration_value:28.6 (24.2-33.0)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Juvenile myoclonic epilepsy (JME)

biospecimen:Blood

concentration_value:30.1 (24.5-35.7)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Acute seizures

biospecimen:Blood

concentration_value:37.2 (34.6-39.8)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Refractory localization-related epilepsy (RLE)

biospecimen:Blood

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Blood

concentration_value:209.0 +/- 46.0

concentration_units:uM

patient_age:Elderly (>65 years old)

patient_sex:Both

patient_information:Alzheimer's Disease

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.31 +/- 0.06

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Parkinson's Disease

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:7.8 +/- 2.5

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Alzheimer's disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Urine

concentration_value:136.5-79.36

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Cystinuria

biospecimen:Urine

concentration_value:90.800-558.500

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystinuria

biospecimen:Urine

concentration_value:140.0813-306.845

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Cystinuria Type I/III

biospecimen:Urine

concentration_value:100.0581-246.245

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Cystinuria Type I/III

biospecimen:Urine

concentration_value:111.929-196.724

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Cystinuria Type II

biospecimen:Urine

concentration_value:11.306-67.836

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Cystinuria Type III

biospecimen:Urine

concentration_value:65.0 (30.0-100.0)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystinuria

biospecimen:Urine

concentration_value:575.0 (150.0 -1000.0)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Cystinuria

biospecimen:Urine

concentration_value:> 117

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystinuria

biospecimen:Urine

concentration_value:908-5585

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hyperlysinuria

biospecimen:Urine

concentration_value:4.423-24.136

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Dibasic Amino Aciduria I

biospecimen:Urine

concentration_value:6.681-21.125

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Dibasic Amino Aciduria I

biospecimen:Urine

concentration_value:0

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Molybdenum cofactor deficiency

biospecimen:Urine

concentration_value:7

concentration_units:umol/mmol creatinine

patient_age:Newborn (0-30 days old)

patient_sex:Not Specified

patient_information:Molybdenum cofactor deficiency

biospecimen:Urine

concentration_value:135.900-156.400

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:Fumaric aciduria

biospecimen:Urine

concentration_value:17.486 +/- 14.104

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Eosinophilic esophagitis

biospecimen:Urine

concentration_value:463.1

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystinuria

biospecimen:Urine

concentration_value:5.975-24.136

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Female

patient_information:Hyperdibasic aminoaciduria I

biospecimen:Urine

concentration_value:6.681-2.305

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hyperdibasic aminoaciduria I

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Urine

concentration_value:72.03 +/- 12.0

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Alzheimer's disease

疾病参考
Juvenile myoclonic epilepsy|Acute seizures|Refractory localization-related epilepsy|Alzheimer's disease|Colorectal cancer|Schizophrenia|Parkinson's disease|Cystinuria|Eosinophilic esophagitis|Molybdenum cofactor deficiency|Fumarase deficiency|Hyperdibasic aminoaciduria I|Hyperlysinuria|

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