gamma-Aminobutyric acid
名称
gamma-Aminobutyric acid
case号
56-12-2
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
细胞
Extracellular|Lysosome|Mitochondria|
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Saliva|Urine|
组织
Adrenal Cortex|Brain|Epidermis|Fibroblasts|Kidney|Neuron|Placenta|Skeletal Muscle|Spleen|Testis|
正常浓度
biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.110 +/- 0.023

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.120-0.500

concentration_units:uM

subject_age:Children (1 - 13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.24 +/- 0.096

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.0200-0.100

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.32 (0.2 -0.45)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.23 +/- 0.075

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.233 +/- 0.075

concentration_units:uM

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.093 (0.083-0.10)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Children (6 - 18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Not Specified

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:4363.856 (2909.238-5818.475)

concentration_units:nmol/g wet feces

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:6658.922 (2812.263-10505.580)

concentration_units:nmol/g wet feces

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:4202.232 (2359.715-6044.749)

concentration_units:nmol/g wet feces

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Feces

concentration_value:576.999 +/- 520.754

concentration_units:nmol/g wet feces

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:>10

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:1.23 +/- 0.57

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:<0.68

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.09 +/- 0.10

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<0.461

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<0.57

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13-18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:8.037 +/- 2.502

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.17 +/- 0.025

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:0.25 +/- 0.20

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:<0.57

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:1.3 (0.0-2.8)

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<2.83

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:<1.47

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:103.89 (72.43 鈥?169.51)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.26 +/- 10.18

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:4.52 +/- 18.09

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<1.24

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:17-20

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:2.9 (2.7-3.3)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:0.46 +/- 0.11

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hepatic encephalopathy

biospecimen:Blood

concentration_value:1.0 (0.0-2.0)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Gaba-transaminase deficiency

biospecimen:Blood

concentration_value:1.45 (0.00-2.9)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:GABA transaminase deficiency

biospecimen:Blood

concentration_value:1.84 +/- 0.215

concentration_units:uM

patient_age:Elderly (>65 years old)

patient_sex:Both

patient_information:Alzheimer's disease

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.13 +/- 0.043

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Spinocerebellar degeneration

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.011

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Female

patient_information:Hyperekplexia

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:1.5 +/- 1.1

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Epilepsy

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.1 (0.063 - 0.179)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Febrile seizure

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.52 - 0.57

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Epilepsy

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.11 (0.067 - 0.176)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Epilepsy

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.05 (0.00-0.10)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Gaba-transaminase deficiency

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:2.4 (0.00-4.8)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:GABA transaminase deficiency

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.1 (0.061 - 0.171)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Meningitis

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.016

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:Typical pyridoxine-dependent seizures

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:4.0 +/- 4.2

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Epilepsy

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.0002 +/- 0.000013

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Tuberculous meningitis

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.00013 +/- 0.00002

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Meningitis

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Crohns disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Ulcerative colitis

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Unclassified IBD

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Not Specified

patient_sex:Not Specified

patient_information:Cryptosporidium infection

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Irritable bowel syndrome

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal Cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Oral cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Female

patient_information:Breast cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Pancreatic cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Periodontal diseases

biospecimen:Saliva

concentration_value:1.08 +/- 0.34

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Male

patient_information:Alzheimer's disease

biospecimen:Saliva

concentration_value:1.78 +/- 0.50

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Male

patient_information:Frontotemporal lobe dementia

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Oral squamous cell carcinoma (OSCC)

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Oral leukoplakia (OLK)

biospecimen:Saliva

concentration_value:5.46 +/- 5.62

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Lewy body disease

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Bladder cancer

biospecimen:Urine

concentration_value:24.545 +/- 17.404

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Eosinophilic esophagitis

biospecimen:Urine

concentration_value:0.75 (0.00-1.50)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Hyper beta-alaninemia

biospecimen:Urine

concentration_value:3.0 (1.5-4.5)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Hyper beta-alaninemia

biospecimen:Urine

concentration_value:118.51 (63.24 鈥?247.72)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Type 1 diabetes Mellitus

疾病参考
Alzheimer's disease|Hepatic encephalopathy|Gaba-transaminase deficiency|Tuberculous meningitis|Meningitis|Epilepsy|Febrile seizures|Pyridoxine-dependent epilepsy|Hyperekplexia|Irritable bowel syndrome|Colorectal cancer|Crohn's disease|Ulcerative colitis|Perillyl alcohol administration for cancer treatment|Pancreatic cancer|Periodontal disease|Frontotemporal dementia|Lewy body disease|Hyper beta-alaninemia|Diabetes mellitus type 1|Eosinophilic esophagitis|
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