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L-Cystathionine
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Urine|
组织
Brain|Kidney|Liver|Prostate|
正常浓度
biospecimen:Blood
concentration_value:0.329 (0.150-0.661)
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0.0440-0.342
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Blood
concentration_value:0.17 (0.1 鈥?0.27)
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:1.0 (0.3-5.5)
concentration_units:uM
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0.126 (0.065 - 0.301)
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:0.024 +/- 0.006
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Children (6 - 18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.84 (0.39-3.28)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<2.036
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<4.98
concentration_units:umol/mmol creatinine
subject_age:Adolescent (13-18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:0.94-2.3
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:14.7 (3.9-20.7)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<3.39
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<34.16
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:0.80-1.6
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:<6.33
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:0-17
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:32.79 +/- 27.13
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:36.18 +/- 35.05
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:41.83 +/- 32.79
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:1.54 卤 1.09
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<2.94
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:0.35 +/- 0.65
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:0.552
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Male
patient_information:Hypermethioninemia
biospecimen:Blood
concentration_value:10
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Blood
concentration_value:1.56 (0.14 - 4.1)
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Folate Deficiency
biospecimen:Blood
concentration_value:0.82 (0.21 - 2.9)
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cobalamin Deficiency
biospecimen:Blood
concentration_value:0.14 (0.04-0.2)
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Autism
biospecimen:Blood
concentration_value:1.03 +/- 0.22
concentration_units:uM
patient_age:Elderly (>65 years old)
patient_sex:Both
patient_information:Alzheimer's disease
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Children (6 - 18 years old)
patient_sex:Not Specified
patient_information:Crohns disease
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Children (6 - 18 years old)
patient_sex:Not Specified
patient_information:Ulcerative colitis
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Children (6 - 18 years old)
patient_sex:Not Specified
patient_information:Unclassified IBD
biospecimen:Urine
concentration_value:6.139
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:6.897
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:182.14
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:84.795
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:216.623
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:381.0 +/- 29.0
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:5.3 (1.0-9.6)
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Cystathioninuria
biospecimen:Urine
concentration_value:1001.0 (158.0-1843.8)
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Gamma-Cystathionase deficiency
biospecimen:Urine
concentration_value:12.677 +/- 3.531
concentration_units:umol/mmol creatinine
patient_age:Children (1 - 13 years old)
patient_sex:Not Specified
patient_information:Eosinophilic esophagitis
biospecimen:Urine
concentration_value:1.68 +/- 0.5
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Alzheimer's disease
疾病参考
Folate deficiency|Vitamin B12 deficiency|Alzheimer's disease|Autism|Hypermethioninemia|Crohn's disease|Ulcerative colitis|Cystathioninuria|Eosinophilic esophagitis|