L-Cystathionine
名称
L-Cystathionine
case号
56-88-2
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
细胞
Cytoplasm|
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Urine|
组织
Brain|Kidney|Liver|Prostate|
正常浓度
biospecimen:Blood

concentration_value:0.329 (0.150-0.661)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.0440-0.342

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:0.17 (0.1 鈥?0.27)

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:1.0 (0.3-5.5)

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.126 (0.065 - 0.301)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.024 +/- 0.006

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Children (6 - 18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.84 (0.39-3.28)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<2.036

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:<4.98

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13-18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.94-2.3

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Urine

concentration_value:14.7 (3.9-20.7)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<3.39

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:<34.16

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.80-1.6

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:<6.33

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0-17

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:32.79 +/- 27.13

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:36.18 +/- 35.05

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:41.83 +/- 32.79

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:1.54 卤 1.09

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<2.94

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:0.35 +/- 0.65

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:0.552

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Hypermethioninemia

biospecimen:Blood

concentration_value:10

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Blood

concentration_value:1.56 (0.14 - 4.1)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Folate Deficiency

biospecimen:Blood

concentration_value:0.82 (0.21 - 2.9)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cobalamin Deficiency

biospecimen:Blood

concentration_value:0.14 (0.04-0.2)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Autism

biospecimen:Blood

concentration_value:1.03 +/- 0.22

concentration_units:uM

patient_age:Elderly (>65 years old)

patient_sex:Both

patient_information:Alzheimer's disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Crohns disease

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Ulcerative colitis

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Children (6 - 18 years old)

patient_sex:Not Specified

patient_information:Unclassified IBD

biospecimen:Urine

concentration_value:6.139

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:6.897

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:182.14

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:84.795

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:216.623

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:381.0 +/- 29.0

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:5.3 (1.0-9.6)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Cystathioninuria

biospecimen:Urine

concentration_value:1001.0 (158.0-1843.8)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Gamma-Cystathionase deficiency

biospecimen:Urine

concentration_value:12.677 +/- 3.531

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Not Specified

patient_information:Eosinophilic esophagitis

biospecimen:Urine

concentration_value:1.68 +/- 0.5

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Alzheimer's disease

疾病参考
Folate deficiency|Vitamin B12 deficiency|Alzheimer's disease|Autism|Hypermethioninemia|Crohn's disease|Ulcerative colitis|Cystathioninuria|Eosinophilic esophagitis|
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