Pipecolic acid
名称
Pipecolic acid
case号
535-75-1
化学分类
Organic compounds
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic heteromonocyclic compounds
细胞
Cytoplasm|Extracellular|
生物样本
Amniotic Fluid|Blood|Cerebrospinal Fluid (CSF)|Feces|Saliva|Urine|
组织
Intestine|Liver|Placenta|Prostate|
正常浓度
biospecimen:Amniotic Fluid

concentration_value:4.65 (2.24 - 8.40)

concentration_units:uM

subject_age:Not Specified

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:2.46 +/- 1.26

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0-5

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0-5

concentration_units:uM

subject_age:Infant (1 - 3 months old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:5.73 (3.75 - 10.8)

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0-10

concentration_units:uM

subject_age:Children (3 months - 6 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0-10

concentration_units:uM

subject_age:Children (6 - 18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:1.46 (0.70-2.46)

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:<4

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:2.0 +/- 0.8

concentration_units:uM

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:0.4-4.9

concentration_units:uM

subject_age:Infant (0-1 year old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Blood

concentration_value:<2.323

concentration_units:uM

subject_age:Children (1 - 13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Blood

concentration_value:<3

concentration_units:uM

subject_age:Children (1 - 13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Blood

concentration_value:0.540-2.460

concentration_units:uM

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:0.774-54.198

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:10.0 (0.0-20.0)

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:1.20 +/- 0.11

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Blood

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Female

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.75 (0.0-1.5)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:<1.5

concentration_units:uM

subject_age:Children (1 - 13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.056 (0.009 - 0.120)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.08 (0.07-0.10)

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.017 +/- 0.005

concentration_units:uM

subject_age:Adult (>18 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:<1.6

concentration_units:uM

subject_age:Children (1-13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0-0.15

concentration_units:uM

subject_age:Children (0 - 10 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0-0.15

concentration_units:uM

subject_age:Adolescent (>11 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:61.166 +/- 74.328

concentration_units:nmol/g wet feces

subject_age:Not Specified

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Feces

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Saliva

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:0.28 (0.0-0.56)

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.03 +/-0.07

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.032

concentration_units:umol/mmol creatinine

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:<0.565

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 13 years old)

subject_sex:Male

subject_condition:Normal

biospecimen:Urine

concentration_value:<6

concentration_units:umol/mmol creatinine

subject_age:Children (1-13 years old)

subject_sex:Not Specified

subject_condition:Normal

biospecimen:Urine

concentration_value:< 0.566

concentration_units:umol/mmol creatinine

subject_age:

subject_sex:

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 25.33

concentration_units:umol/mmol creatinine

subject_age:Newborn (0-30 days old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 13.91

concentration_units:umol/mmol creatinine

subject_age:Infant (1 - 6 months old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 5.09

concentration_units:umol/mmol creatinine

subject_age:Infant (6 months - <1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 0.64

concentration_units:umol/mmol creatinine

subject_age:Children (1 - 2 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 0.64

concentration_units:umol/mmol creatinine

subject_age:Children (2 - 4 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 0.64

concentration_units:umol/mmol creatinine

subject_age:Children (4 - 13 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 0.64

concentration_units:umol/mmol creatinine

subject_age:Adolescent (13 - 21 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0 - 0.64

concentration_units:umol/mmol creatinine

subject_age:Adult (>21 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:0.03 +/- 0.07

concentration_units:umol/mmol creatinine

subject_age:Infant (0-1 year old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

biospecimen:Urine

concentration_value:

concentration_units:

subject_age:Adult (>18 years old)

subject_sex:Both

subject_condition:Normal

异常浓度
biospecimen:Blood

concentration_value:39.6

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Both

patient_information:Infantile Refsum disease

biospecimen:Blood

concentration_value:79.0 (5.0 - 378.0)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Peroxisomal biogenesis defect

biospecimen:Blood

concentration_value:2.8-23

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:Pyridoxine dependency with seizures (PDE)

biospecimen:Blood

concentration_value:2.3

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:Pseudo Zellweger->D-bifunctional protein deficiency

biospecimen:Blood

concentration_value:0-1.66

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Pseudoneonatal adrenoleukodystrophy

biospecimen:Blood

concentration_value:4.1

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Female

patient_information:Rhizomelic chondrodysplasia punctata

biospecimen:Blood

concentration_value:9.22

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Not Specified

patient_information:Zellweger syndrome

biospecimen:Blood

concentration_value:21

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Male

patient_information:Peroxisomal biogenesis disorder

biospecimen:Blood

concentration_value:<3.871

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Adrenoleukodystrophy, X-linked

biospecimen:Blood

concentration_value:<3.871

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Not Specified

patient_information:Refsum disease, classic, adult-onset

biospecimen:Blood

concentration_value:0-1.660

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Not Specified

patient_information:Neonatal adrenoleukodystrophy

biospecimen:Blood

concentration_value:0-38.713

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Refsum disease, juvenile

biospecimen:Blood

concentration_value:15-64

concentration_units:uM

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:Infantile Refsum disease

biospecimen:Blood

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

biospecimen:Blood

concentration_value:170.335-185.820

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Refsum disease, infantile

biospecimen:Blood

concentration_value:232.275-363.898

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Peroxisomal disorders, new type, liver

biospecimen:Blood

concentration_value:26.325-216.790

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Both

patient_information:Zellweger syndrome

biospecimen:Blood

concentration_value:27.0988-162.593

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Both

patient_information:Neonatal adrenoleukodystrophy

biospecimen:Blood

concentration_value:38.712-154.85

concentration_units:uM

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:Infantile Refsum's disease

biospecimen:Blood

concentration_value:4.120-280

concentration_units:uM

patient_age:Newborn (0-30 days old)

patient_sex:Female

patient_information:Peroxisomal biogenesis disorder

biospecimen:Blood

concentration_value:60.860-62.100

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Female

patient_information:Peroxisomal biogenesis disorder

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:1.8

concentration_units:uM

patient_age:Infant (0-1 year old)

patient_sex:Both

patient_information:Infantile Refsum disease

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:<0.5 - 3.5

concentration_units:uM

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:Infantile Refsum disease

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.053 (0.023-0.083)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Brain injury

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.19 (0.17-0.21)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Malaria

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.38 (0.11-1.26)

concentration_units:uM

patient_age:Not Specified

patient_sex:Not Specified

patient_information:Anemia

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.18 (0.14-0.22)

concentration_units:uM

patient_age:Not Specified

patient_sex:Not Specified

patient_information:Malaria

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.17 (0.12-0.23)

concentration_units:uM

patient_age:Not Specified

patient_sex:Not Specified

patient_information:Tuberculous meningitis

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.06 (0.02-0.26)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Malaria

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:24-33

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Hyperlysinemia I, familial

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:0.05 (0.02-0.09)

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Convulsions

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:1-2

concentration_units:uM

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Hyperpipecolatemia

biospecimen:Cerebrospinal Fluid (CSF)

concentration_value:1.715 (0.33 - 3.10)

concentration_units:uM

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Peroxisomal biogenesis defect

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal cancer

biospecimen:Feces

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Colorectal Cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Male

patient_information:Periodontal Probing Depth

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Oral cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Female

patient_information:Breast cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Pancreatic cancer

biospecimen:Saliva

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Not Specified

patient_information:Periodontal diseases

biospecimen:Urine

concentration_value:2.0

concentration_units:umol/mmol creatinine

patient_age:Infant (0-1 year old)

patient_sex:Both

patient_information:Infantile Refsum disease

biospecimen:Urine

concentration_value:3.3 (1.5-5.0)

concentration_units:umol/mmol creatinine

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Adrenoleukodystrophy

biospecimen:Urine

concentration_value:49.4 (8.4-90.4)

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Adrenoleukodystrophy (ALD)

biospecimen:Urine

concentration_value:0.02-228.3

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Not Specified

patient_information:Zellweger Syndrome

biospecimen:Urine

concentration_value:0-5.314

concentration_units:umol/mmol creatinine

patient_age:Children (1 - 13 years old)

patient_sex:Male

patient_information:Infantile Refsum disease

biospecimen:Urine

concentration_value:0.93-70

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Both

patient_information:Pseudoneonatal adrenoleukodystrophy

biospecimen:Urine

concentration_value:4.522

concentration_units:umol/mmol creatinine

patient_age:Children (1-13 years old)

patient_sex:Male

patient_information:Hyperpipecolatemia

biospecimen:Urine

concentration_value:

concentration_units:

patient_age:Adult (>18 years old)

patient_sex:Both

patient_information:Schizophrenia

疾病参考
Infantile Refsum's disease|Rhizomelic chondrodysplasia punctata|Refsum's disease|Peroxisomal disorders, new type, liver|Pyridoxine-dependent epilepsy|D-Bifunctional protein deficiency|Pseudoneonatal adrenoleukodystrophy|Traumatic brain injury|Malaria|Anemia|Tuberculous meningitis|Convulsion|Hyperlysinemia I, familial|Hyperpipecolatemia|Colorectal cancer|Perillyl alcohol administration for cancer treatment|Pancreatic cancer|Periodontal disease|Periodontal Probing Depth|Peroxisomal biogenesis defect|Adrenoleukodystrophy|Schizophrenia|

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