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Argininosuccinic acid
子类
Organic acids and derivatives
细胞类型
Carboxylic acids and derivatives
子类
Amino acids, peptides, and analogues
化学架构
Aliphatic acyclic compounds
组织
Kidney|Placenta|Prostate|
正常浓度
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:<2
concentration_units:uM
subject_age:Infant (0-1 year old)
subject_sex:Male
subject_condition:Normal
biospecimen:Blood
concentration_value:0-5
concentration_units:uM
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0-5
concentration_units:uM
subject_age:Infant (1 - 3 months old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0-5
concentration_units:uM
subject_age:Children (3 months - 6 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0-5
concentration_units:uM
subject_age:Children (6 - 18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:0-1
concentration_units:uM
subject_age:Children (1 - 13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<2.71
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<7.81
concentration_units:umol/mmol creatinine
subject_age:Adolescent (13-18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<4
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:<1.70
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<8.71
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<0.433
concentration_units:umol/mmol creatinine
subject_age:Not Specified
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:<5.43
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Not Specified
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:<4.19
concentration_units:umol/mmol creatinine
subject_age:Children (1-13 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Urine
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0-99
concentration_units:umol/mmol creatinine
subject_age:Newborn (0-30 days old)
subject_sex:Both
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:1515
concentration_units:uM
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Argininosuccinic aciduria (ASL)
biospecimen:Blood
concentration_value:300.0 (270.0-458.0)
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Argininosuccinyl-CoA lyase deficiency
biospecimen:Urine
concentration_value:667
concentration_units:umol/mmol creatinine
patient_age:Infant (0-1 year old)
patient_sex:Male
patient_information:Argininosuccinic aciduria (ASL)
biospecimen:Urine
concentration_value:0.65 (0.0-1.3)
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Argininemia
biospecimen:Urine
concentration_value:1542.00
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Argininosuccinic aciduria (ASL)
疾病参考
Argininosuccinyl-CoA lyase deficiency|Argininemia|Argininosuccinic aciduria|