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alpha-Ketoisovaleric acid
名称
alpha-Ketoisovaleric acid
子类
Organic acids and derivatives
细胞类型
Keto acids and derivatives
子类
Short-chain keto acids and derivatives
化学架构
Aliphatic acyclic compounds
细胞
Cytoplasm|Extracellular|Membrane|Mitochondria|
生物样本
Blood|Cerebrospinal Fluid (CSF)|Feces|Saliva|Urine|
正常浓度
biospecimen:Blood
concentration_value:14.0 (0.0-28.0)
concentration_units:uM
subject_age:Children (1-13 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:11.0 +/- 1.7
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Blood
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:6 +/- 3
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:8.2 +/- 6.8
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Feces
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Saliva
concentration_value:0.679 +/- 0.369
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Saliva
concentration_value:0.752 +/- 0.287
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Saliva
concentration_value:1.06 +/- 0.436
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Not Specified
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:
concentration_units:
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:0.345 +/- 0.858
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Saliva
concentration_value:0.434 +/- 0.382
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Saliva
concentration_value:0.656 +/- 0.399
concentration_units:uM
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:0.78-1.2
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:0.16 +/- 0.48
concentration_units:umol/mmol creatinine
subject_age:Infant (0-1 year old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.5 (0.2-1.1)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Both
subject_condition:Normal
biospecimen:Urine
concentration_value:0.13 (0.00-0.54)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0.07 (0.01-0.45)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
biospecimen:Urine
concentration_value:0.79-1.1
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Male
subject_condition:Normal
biospecimen:Urine
concentration_value:0.07 (0.01-0.45)
concentration_units:umol/mmol creatinine
subject_age:Adult (>18 years old)
subject_sex:Female
subject_condition:Normal
异常浓度
biospecimen:Blood
concentration_value:10.7 +/- 5.5
concentration_units:uM
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Heart Transplant
biospecimen:Blood
concentration_value:237
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Maple syrup urine disease
biospecimen:Cerebrospinal Fluid (CSF)
concentration_value:189
concentration_units:uM
patient_age:Children (1-13 years old)
patient_sex:Female
patient_information:Maple syrup urine disease
biospecimen:Feces
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Colorectal Cancer
biospecimen:Urine
concentration_value:
concentration_units:
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Bladder cancer
biospecimen:Urine
concentration_value:550.00 (300.00-800.00)
concentration_units:umol/mmol creatinine
patient_age:Adult (>18 years old)
patient_sex:Both
patient_information:Maple syrup urine disease (MSUD). When treated, the concentrations are 1-2 uM/mM.
biospecimen:Urine
concentration_value:550.00 (300.00-800.00)
concentration_units:umol/mmol creatinine
patient_age:Children (1-13 years old)
patient_sex:Both
patient_information:Maple syrup urine disease (MSUD). When treated, the concentrations are 1-2 uM/mM.
疾病参考
Colorectal cancer|Maple syrup urine disease|